Congenital vascular disorders characterized by triads include: Vein or vein defects, vascular malformations, and wine color reduction due to abnormal capillary reproduction in one or more liaos.
1. Congenital vascular syndrome
Congenital vascular syndrome, also known as klippel-trenaunay syndrome, affects both men and women at an equal rate, and is not limited to one race.
Several trials have shown that congenital vascular disorders are associated with genetic transcriptation, but there is still no accurate determination of genetic nature.
2. Symptoms of congenital vascular syndrome
Currently, the exact cause of congenital vascular disorders has not been determined. Therefore, in order to determine the syndrome, it is necessary to combine with the symptoms of manifestations of the disease including:
- One or more red wine pigmentation appears.
- The veins are dilated.
- Bone hypertrophy and soft tissue, which can lead to local atrophy or enormous deformation of some parts.
- Abnormal development of the lymphatic system.
These symptoms usually affect about 1⁄4 of the body, in some cases may be narrow or wider. And in rare cases may not be accompanied by pigmentation plaques, capillary pigmentation, which is called atypical congenital vascular syndrome.
In addition, congenital vascular disorders can affect the vascular system and lymphatic system or both. The most common is the form that affects both systems. The quality of life of a person with damage to the vein system is usually lower because the person often has aches and pains and has more complications.
For people with arterial malformation, large veins are at risk of thrombosis and may go up the lungs leading to pulmonary embolism. If a large blood flow passes through the lesion area, high output heart failure may occur, as the heart loses its ability to meet a sufficient heart supply.
3. Treatment of congenital vascular disorders
Treatment of congenital vascular disorders has many methods such as:
3.1 Surgical methods
Surgical reduction of deformities is a method that has been widely used for many years. However, this measure is heavily invasive, can have many complications and a high rate of recurrence of the disease.
3.2 Conservative treatment
- Fibrosis: Is a treatment for less invasive congenital vascular disorders than surgery. However, the recurrence rate of treatment with this method is quite high, in some cases it does not bring results, if there are large malformations with arterial fistula.
- Embolism: Is a measure that can slow down the development of deformities, support with fibrous injection methods, surgery. Embolism is used if it is detected with a fistula, veins when an anemones.
- Wear pressure socks or elastic bandages: Is one of the most used remedies over the years, especially for children. Although the effectiveness of this method has not been proven specifically, due to its simplicity, less invasiveness, fewer complications and convenience, it still has a certain role to play.
Congenital vascular syndrome (Klippel – Trenaunay – Weber) is a complex congenital abnormality. Currently, there is not yet a specific treatment but mainly focuses on treating symptoms. Depending on the specific case and the treatment point of view of each specialist, the course of treatment can coordinate one or more different measures.
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